The Klippel Feil deformity is a complex of osseous and visceral anomalies that includes low hair line, platybasia, fused cervical vertebra with short neck and deafness along with involvement of other systems. The bony malformations may entrap and damage the brain and spinal cord. The disorders of the lower vertebral region may become symptomatic with rapid growth seen in adolescence or in adult life. Here we present a six year boy with purely skeletal deformities without any other visceral abnormalities.