文章基本信息

标题：Systemic Mastocytosis With Features of Chronic Liver Disease, Proptosis and Itchy Hyper-Pigmented Skin Lesion
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作者：Benzamin ; Rafiqul Islam ; Mukesh Khadga 等
期刊名称：KYAMC Journal
印刷版ISSN：2308-2860
出版年度：2020
卷号：11
期号：1
页码：50-53
DOI：10.3329/kyamcj.v11i1.47152
出版社：Khwaja Yunus Ali Medical College and Hospital
摘要：Mastocytosisis a rare disorder of functionally defective mast cells. Infiltration of this functionally defective mast cells and CD34 mast cell precursors in various organ leads to clinical manifestation. Skin is the most common affected organ. In systemic mastocytosis along with skin, internal organs such as the liver, spleen, bone marrow, small intestines and eye also involve. Diagnosis is done on the basis of WHO diagnostic criteria. Here we presenting this rare entity presented to us with features of chronic liver disease, proptosis and itchy hyperpigmented skin lesion diagnosed as systemic mastocytosis.
关键词：Mastocytosis;Mast cells;Proptosis;Chronic Liver Disease