摘要:Background: The occurrence of an extra-uterine leiomyoma, arising from the intra-peritoneal portion of the round
ligament in a lady with Müllerian agenesis diagnosed at the age of forty is extremely rare. We report a case of this
rare combination in a Middle Eastern woman.
Case: A 40 years old lady, primarily amenorrheic, presented to our clinic for an infertility consultation. The workup
showed features suggestive of Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome with a leiomyoma arising
from the intra-peritoneal part of the round ligament.