摘要:Aortopulmonary window, an aortopulmonary septal defect, is a rare congenital heart defect in which there is a communication between the ascending aorta and pulmonary trunk in the presence of 2 normally separate semilunar valves. There is often undetected in prenatal period, with considerable morbidity and mortality if undiagnosed. The clinical presentation is dependent upon the size of the defect, associated abnormalities, and the presence or absence of elevated pulmonary vascular resistance. We present a case of a 21-year-old pregnant patient with no family history of any congenital heart disease who was referred for fetal echocardiography evaluation at 31 weeks’ gestation due to suspected cardiac anomaly. On ultrasound, heart showed normal position and size. There was found in three-vessel view a gap between the pulmonary artery and the aorta. The size of the defect was 5 millimeters. Fetal echocardiography showed an aortopulmonary septum defect and a left - right flow was detected by color flow Doppler. The diagnosis was considered to be an aortopulmonary window. An atrial septal defect with shunt left - right was also found. The result of karyotype analysis was normal without 22q11 deletion. The prenatal diagnosis was confirmed by postnatal echocardiography. After 4 days of life, a total surgical correction was accomplished. Early neonatal surgery was successful.