文章基本信息

标题：Uncommon presentations of an uncommon entity: OHVIRA syndrome with hematosalpinx and pyocolpos
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作者：Z. Sleiman ; T. Zreik ; R. Bitar 等
期刊名称：Facts, Views & Vision in ObGyn
印刷版ISSN：2032-0418
出版年度：2017
卷号：9
期号：3
页码：167-170
出版社：Universa Press
摘要：Müllerian malformations result from defective fusion of the Müllerian ducts during development of the femalereproductive system. The least common form of these malformations is Herlyn-Werner-Wunderlich syndromecharacterized by obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). The most common presentationof this syndrome is a mass secondary to hematocolpos, pain, and dysmenorrhea. Clinical diagnosis is verychallenging and requires imaging studies in which ultrasound and MRI play an essential role in the diagnosis,classification and treatment plan.We report two cases of this syndrome, featuring two very rare clinical presentations: hematosalpinx and pyocolpos.The clinical course of the pathology is not standard and each patient is treated accordingly.
关键词：OHVIRA; pyocolpos; hematosalpinx; hysteroscopy; laparoscopy; MRI; ultrasound.